Fast Five Quiz: Fibrodysplasia Ossificans Progressiva

Dirk M. Elston, MD


January 14, 2021

In large part, management of FOP is centered on strategies that prevent flare-ups: taking precautions against falls, respiratory decline, and viral infections. Physical rehabilitation should enhance activities of daily living while avoiding passive range of motion.

In children, although restricting activity may protect against falls, overly stringent precautions may prevent them from optimizing their level of function and compromise their independence.

Because deep-tissue trauma may lead to irreversible damage, intramuscular injections should be avoided.

For stabilization and procedures, venipuncture, subcutaneous medications, and intravenous medications are acceptable.

Patients with FOP may require oral surgical and anesthetic procedures to control oral pain. In these instances, a minimally invasive surgical technique and appropriate anesthetic management are critical to protect the jaw. Awake nasal fiberoptic intubation is considered desirable for airway management. Expert anesthesiologist consultation is important.

Learn more about treatment and management of FOP.

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