Fast Five Quiz: Interstitial Lung Disease Progressive Fibrosing Management

Zab Mosenifar, MD


February 01, 2022

Patients with persistent resting hypoxemia PaO2 at or below 7.3 kPa (55 mm Hg) or below 8 kPa with clinical evidence of pulmonary hypertension and who are breathless should be considered for supplemental oxygen.

The main objectives of comprehensive pulmonary rehabilitation include increased independence and improved quality of life, as well as fewer hospitalizations or shorter hospitalization time. Coupled with exercise, a pulmonary rehabilitation program may improve a patient's functional status. However, these activities generally do not slow disease progression. Pulmonary rehabilitation does not reverse airway obstruction or hyperinflation associated with COPD, but it does allow for reversal of muscle deconditioning, ultimately enabling patients to walk farther and with less dyspnea.

Comorbid conditions associated with fibrosing ILD include pulmonary hypertension, gastroesophageal reflux disease, obesity, emphysema, and obstructive sleep apnea. Whether treating these comorbidities can influence clinical outcomes remains an open question.

Pulmonary function testing may be performed every 3-6 months in the course of long-term monitoring.

Learn more about the treatment of PF-ILD.


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