Progressive fibrosing interstitial lung diseases (PF-ILD) are a heterogeneous group of interstitial lung diseases clinically characterized by accelerated respiratory failure, frequent disease exacerbation, and earlier mortality. PF-ILD includes a wide range of diseases with disparities in clinical patterns and disease features. In PF-ILD, progressive fibrosis of the lung parenchyma results in a gradual deterioration in lung function and respiratory symptoms despite conventional treatment. It is estimated that 18%-32% of patients diagnosed with non-IPF-ILD develop progressive fibrosis. Facilitating an accurate diagnosis can improve and extend the lives of patients with PF-ILD and ensure appropriate therapy.
Can you identify PF-ILD? Test your knowledge with this quick quiz.
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Cite this: Zab Mosenifar. Fast Five Quiz: Progressive Fibrosing Interstitial Lung Disease Presentation and Diagnosis - Medscape - Apr 24, 2023.