Fast Five Quiz: Progressive Fibrosing Interstitial Lung Disease Presentation and Diagnosis

Zab Mosenifar, MD

Disclosures

June 16, 2022

Patients with ILD associated with connective tissue disease and fibrotic hypersensitivity pneumonitis appear to have a better prognosis than patients with IPF.

Retrospective studies have identified risk factors for progression and mortality in PF-ILD, including lower diffusing capacity of the lung for carbon monoxide at baseline. Other risk factors include male sex, older age, lower forced vital capacity at baseline, and certain morphologic features, such as a radiologic and/or histologic pattern of usual interstitial pneumonia.

Egan and colleagues proposed a classification scheme of advanced versus limited disease based on a cutoff value of diffusing capacity of the lung for carbon monoxide greater than 40%.

Learn more about staging PF-ILD.

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