Patients with ILD associated with connective tissue disease and fibrotic hypersensitivity pneumonitis appear to have a better prognosis than patients with IPF.
Retrospective studies have identified risk factors for progression and mortality in PF-ILD, including lower diffusing capacity of the lung for carbon monoxide at baseline. Other risk factors include male sex, older age, lower forced vital capacity at baseline, and certain morphologic features, such as a radiologic and/or histologic pattern of usual interstitial pneumonia.
Learn more about staging PF-ILD.
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Cite this: Zab Mosenifar. Fast Five Quiz: Progressive Fibrosing Interstitial Lung Disease Presentation and Diagnosis - Medscape - Jun 16, 2022.