Systemic sclerosis (SSc) is a collagen tissue disorder (CTD) characterized by diffuse fibrosis and vascular abnormalities in the skin, joints, and internal organs. Fibrosing interstitial lung disease (ILD) is a common manifestation of SSc, leading to exertional dyspnea and restrictive lung disease with eventual respiratory failure. ILD is the most common cause of death in patients with SSc, with a 10-year mortality of up to 40%. Diagnosis of SSc-ILD is based on high-resolution CT (HRCT) findings in a patient with known SSc, along with normal or abnormal pulmonary function tests (PFTs). In most cases, the goal of treatment is to achieve disease stabilization.
Are you up-to-date on the management of SSc-ILD? Test your knowledge with this quick quiz.
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Cite this: Zab Mosenifar. Fast Five Quiz: Management of Systemic Sclerosis Interstitial Lung Disease - Medscape - Mar 28, 2023.