Fast Five Quiz: Progressive Fibrosing Interstitial Lung Disease

Zab Mosenifar, MD, FACP, FCCP


April 12, 2022

Corticosteroid therapy may be indicated for acute symptomatic relief of HP and may accelerate the initial recovery in persons with severe disease. Treatment regimens vary according to the prescriber; therapy should be guided by clinical response, pulmonary function, and radiographic improvement. Maintenance doses are not always required, particularly if the patient is removed from exposure.

Outside of oral corticosteroids, several other alternative therapies have been explored in select cases. Inhaled corticosteroids, bronchodilators, cromolyn sodium, and antihistamines may be helpful in cases with obstructive physiology with reversibility.

The use of low-dose macrolide antibiotics has been suggested for inflammation reduction, but beneficial effects have not been verified.

The use of immunosuppressive agents such as azathioprine or cyclosporine has been documented in select pediatric cases but not in the adult population.

Learn more about the treatment and management of HP.

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