Fast Five Quiz: Inherited Retinal Diseases

Raj K. Maturi, MD

Disclosures

March 31, 2023

According to the AAO, patients with advanced IRDs may have unstable, eccentric fixation that may challenge the interpretation of static perimetry and microperimetry. As such, the value of these tests in following patients with advanced disease is uncertain.

All patients with IRDs should be seen for regular follow-up, at least once per year, or more often as indicated. Goldmann visual field and visual acuity should be measured during follow-up examinations. There may be benefits to treatment of central cystoid macular edema in patients with retinitis pigmentosa. Topical nonsteroidal drops or carbonic anhydrase inhibitors can be beneficial in these cases. A delay in performing cataract surgery may be appropriate in certain cases, as these patients are at a high risk of developing cystoid macular edema postoperatively.

Optical coherence tomography angiography is emerging as a noninvasive modality for characterizing various IRDs as well as stages of IRD progression. However, the AAO states that it is not currently recommended for monitoring disease progression in patients with IRDs.

Learn more about follow-up in IRDs.

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